Porokeratosis: clinical manifestations and treatment options
https://doi.org/10.33667/2078-5631-2020-6-87-90
Abstract
Porokeratosis is a rare disease with an autosomal dominant type of inheritance. It is customary to distinguish classic Mibelli porokeratosis, as well as disseminated and localized variations of the course of dermatosis, which differ in genetic predisposition, trigger factors, and treatment approaches. The article describes the variants of the disease – eruptive itchy papular malformation that occurs on the extremities against the background of microcirculation disorders and giant, developed on the skin of the trunk. The main methods of treatment of porokeratosis are also described.
About the Authors
A. B. Yakovlev
Central State Medical Academy of the Administrative Department of the President of Russia
Russian Federation
Russian Federation
Moscow
O. A. Golanova
Central State Medical Academy of the Administrative Department of the President of Russia
Russian Federation
Russian Federation
Moscow
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For citations:
Yakovlev A.B., Golanova O.A. Porokeratosis: clinical manifestations and treatment options. Medical alphabet. 2020;(6):87-90. (In Russ.) https://doi.org/10.33667/2078-5631-2020-6-87-90
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