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Clinical case of a giant extragastrointestinal tumor of the retroperitoneum and review of the literature

https://doi.org/10.33667/2078-5631-2024-17-38-42

Abstract

Extragastrointestinal stromal tumors (EGIST) are rare lesions in the mesenchymal neoplasm, accounting for less than 1% of the primary neoplasias of the digestive tract. In only 10% of the cases EGIST may affect any segment of the gastrointestinal tract and can occur in other locations (omentum, mesentery, or retroperitoneum, GIST arising from the pancreas). The incidence is approximately 14.5 patients per 1 million persons [1–3]. To date, more than 190 cases have been published. We reported a rare case of huge mesenteric extra-gastrointestinal stromal tumor presenting as a peritoneal mass in a 53-year-old patient

About the Authors

G. A. Khakimov
Tashkent city filial of Republic Specialized Medical-Practical Center of Oncology and Radiology; Tashkent Pediatric Medical Institute
Uzbekistan

Khakimov Golib A. - DM Sci (habil.), professor, director; head of Dept of Pediatric Oncology

Tashkent



G. G. Khakimova
Tashkent city filial of Republic Specialized Medical-Practical Center of Oncology and Radiology; Tashkent Pediatric Medical Institute
Uzbekistan

Khakimova Gulnoz G. - PhD Med, oncologist at Dept of Chemotherapy; assistant at Dept of Oncology

Tashkent



F. B. Djumanova
Tashkent city filial of Republic Specialized Medical-Practical Center of Oncology and Radiology
Uzbekistan

Djumanova Feruza Bakhodir kizi - graduate student at Dept of Pediatric Oncology

Tashkent



G. P. Orifjonova
Nano Medical Clinic
Uzbekistan

Orifjonova Gulzodakhon Pulatjon kizi - medical oncologist

Tashkent



Sh. Sh. Kadyrov
Tashkent Pediatric Medical Institute; Tashkent city filial of Republic Specialized Medical-Practical Center of Oncology and Radiology
Russian Federation

Kadyrov Sherzod Sh. - assistant at Dept of Pediatric Oncology; Head of the 
thoraco-abdominal department

Tashkent



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Review

For citations:


Khakimov G.A., Khakimova G.G., Djumanova F.B., Orifjonova G.P., Kadyrov Sh.Sh. Clinical case of a giant extragastrointestinal tumor of the retroperitoneum and review of the literature. Medical alphabet. 2024;(17):38-42. (In Russ.) https://doi.org/10.33667/2078-5631-2024-17-38-42

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ISSN 2078-5631 (Print)
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