Electrodiagnostic features of myasthenia gravis in patient with predominantly bulbar symptoms. Case report
https://doi.org/10.33667/2078-5631-2022-33-27-32
Abstract
Myasthenia gravis is an autoimmune disease, the clinical manifestations of which are in the form of weakness and pathological muscle fatigue. We present the clinical case of a patient with predominantly lingual muscle involvement. The patient was diagnosed with a generalized 2A–2B form of myasthenia gravis. Dysarthria and weakness of the masticatory muscles were observed at the onset of the disease. The diagnosis was established 1.5 months after the appearance of the first complaints. Diagnosis at the outpatient stage was hampered by the epidemiological history and the short duration of symptoms that occurred only after eating. All of the above determines the importance of clinician`s alertness about the possibility of this disease manifesting itself in such a rather specific and rare group of symptoms.
About the Authors
E. G. Seliverstova
N. V. Sklifosovsky Research Institute of Emergency Care; City Clinical Hospital n.a. I. V. Davydovsky
Russian Federation
Russian Federation
Ekaterina G. Seliverstova, MD, neurophysiologist, junior researcher
Clinical Neurophysiology Laboratory
Emergency Neurosurgery Deparment
Moscow
M. V. Sinkin
N. V. Sklifosovsky Research Institute of Emergency Care; A. I. Yevdokimov Moscow State University of Medicine and Dentistry
Russian Federation
Russian Federation
Mikhail V. Sinkin, head of the Laboratory
Emergency Neurosurgery Deparment
Clinical Neurophysiology Laboratory
Laboratory of invasive neurointerfaces
Moscow
V. B. Voitenkov
Pediatric Research and Clinical Center for Infectious Diseases; Academy of Postgraduate Education of Federal Scientific Research Center
Russian Federation
Russian Federation
Vladislav B. Voitenkov, PhD, Head of Department, Associate Professor
Clinical Department of Neurophysiology
Neurology Department and Neurorehabilitation
Saint-Petersburg
Moscow
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Review
For citations:
Seliverstova E.G., Sinkin M.V., Voitenkov V.B. Electrodiagnostic features of myasthenia gravis in patient with predominantly bulbar symptoms. Case report. Medical alphabet. 2022;(33):27-32. (In Russ.) https://doi.org/10.33667/2078-5631-2022-33-27-32
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