medalphabetМедицинский алфавитMedical alphabet2078-56312949-2807ООО «Альфмед»10.33667/2078-5631-2024-22-29-33medalphabet-3995Research ArticleСтатьиДиагностика снижения сегментарной деформации миокарда левого желудочка у подростка на ранней стадии гипертрофической кардиомиопатии (клиническое наблюдение)Diagnosis of decreased segmental deformation of the left ventricular myocardium in a teenager at the early stage of hypertrophic cardiomyopathy (clinical observation)https://orcid.org/0000-0002-7511-3240ГрозноваО. С.GroznovaO. S.

Грознова Ольга Сергеевна, д.м.н., главный научный сотрудник отдела детской кардиологии и аритмологии, директор, профессор кафедры инновационной педиатрии и детской хирургии

г. Москва

Groznova Olga Sergeevna, Dr. Med. Sc., сhief Researcher of the Department of Pediatric Cardiology and Arrhythmology, director, Professor of the Department of Innovative Pediatrics and Pediatric Surgery

Moscow

ogroznova@internet.ruhttps://orcid.org/0000-0002-8033-665XТарасоваА. А.TarasovaA. A.

Тарасова Алла Алексеевна, д.м.н., профессор, профессор кафедры лучевой диагностики детского возраста

г. Москва

Tarasova Alla Alekseevna, Dr. Med. Sc., Professor, Professor of the Department of Radiation Diagnostics of children

Moscow

https://orcid.org/0009-0001-6469-3171ВерченкоЕ. Г.VerchenkoE. G.

Верченко Елена Геннадьевна, к.м.н., врач ультразвуковой диагностики отделения функциональной диагностики нарушений сердечного ритма

г. Москва

Verchenko Elena Gennadievna, Cand. Med. Sc., ultrasound diagnostics doctor of the Department of functional diagnostics of cardiac arrhythmias

Moscow

БерезницкаяВ. В.BereznitskayaV. V.

Березницкая Вера Васильевна, к.м.н., заведующая детским кардиологическим отделением нарушений сердечного ритма

г. Москва

Bereznitskaya Vera Vasilievna, Cand. Med. Sc., Head of the Pediatric Cardiology Department of Cardiac Arrhythmias

Moscow

ОСП «НИКИ педиатрии и детской хирургии им. академика Ю.Е. Вельтищева» ФГБОУ ВО «Российский национальный исследовательский медицинский университет имени Н.И. Пирогова» Минздрава РФ; Благотворительный фонд медико-социальных генетических проектов помощи «Геном Жизни»; Кафедра инновационной педиатрии и детской хирургии Института непрерывного образования и профессионального развития ФГБОУ ВО «Российский национальный исследовательский медицинский университет имени Н.И. Пирогова» Минздрава РФРоссияVeltischev Research and Clinical Institute for Pediatrics and Pediatric Surgery of the Pirogov Russian National Research Medical University; Charity Fund for medical and social genetic aid projects «Life Genome»; Department of Innovative Pediatrics and Pediatric Surgery, Institute of Continuing Education and Professional Development of the Pirogov Russian National Research Medical UniversityRussian FederationФГБОУ ДПО «Российская медицинская академия непрерывного профессионального образования» Минздрава РФРоссияRussian Medical Academy of Continuing Professional Education of the Ministry of Health of the Russian FederationRussian FederationОСП «НИКИ педиатрии и детской хирургии им. академика Ю.Е. Вельтищева» ФГБОУ ВО «Российский национальный исследовательский медицинский университет имени Н.И. Пирогова» Минздрава РФРоссияVeltischev Research and Clinical Institute for Pediatrics and Pediatric Surgery of the Pirogov Russian National Research Medical UniversityRussian Federation202404122024022«Современная функциональная диагностика» (3)2933Copyright © Грознова О.С., Тарасова А.А., Верченко Е.Г., Березницкая В.В., 20242024Грознова О.С., Тарасова А.А., Верченко Е.Г., Березницкая В.В.Groznova O.S., Tarasova A.A., Verchenko E.G., Bereznitskaya V.V.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.med-alphabet.com/jour/article/view/3995

В статье представлено клиническое наблюдение, выявившее снижение сегментарной деформации миокарда левого желудочка у подростка 15 лет на ранней стадии асимметричной необструктивной гипертрофической кардиомиопатии (ГКМП). Для оценки систолической функции миокарда исследовались: фракции выброса и укорочения левого желудочка, а также показатели глобальной и сегментарной деформации миокарда, определяемые при эхокардиографическом исследовании в режиме метода 2D speckletracking. Отмечалось отсутствие изменений фракций выброса и укорочения левого желудочка, глобальной продольной деформации миокарда, но при этом наблюдалось снижение продольной и циркулярной деформации в отдельных сегментах левого желудочка, что, в том числе, явилось основанием для назначения кардиопротективной терапии.

The article presents a clinical observation that revealed a decrease in segmental deformation of the left ventricular myocardium in a 15-year-old teenager at the early stage of asymmetric non-obstructive hypertrophic cardiomyopathy (HCM). To assess myocardial systolic function, the following were used: ejection fraction and shortening of the left ventricle, as well as indicators of global and segmental myocardial deformation, determined by echocardiographic study using the 2D speckle-tracking method. There was no change in ejection fractions and shortening of the left ventricle, global longitudinal deformation of the myocardium, but there was a decrease in longitudinal and circular deformation in individual segments of the left ventricle, which, in general, was the basis for prescribing cardioprotective therapy.

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The authors declare that there are no conflicts of interest present.