medalphabetМедицинский алфавитMedical alphabet2078-56312949-2807ООО «Альфмед»10.33667/2078-5631-2023-32-47-49medalphabet-3436Research ArticleСтатьиУльтразвуковая визуализация нейролипоматоза срединного нерва: обзор литературы и описание клинического случаяUltrasound imaging of median nerve neurolipomatosis: literature review and clinical case descriptionhttps://orcid.org/0009-0005-7699-910XХалиловаТ. Е.KhalilovaT. E.

Халилова Татьяна Евгеньевна, заведующая отделением неврологии и психиатрии

Подольск.

Tatiana Evgenievna Khalilova, Head of the Department of Neurology and Psychiatry

Podolsk.

tatyanahalilova@mail.ruhttps://orcid.org/0000-0002-6244-0867ДружининД. С.DruzhininD. S.

Дружинин Д. С., д.м.н., доцент кафедры нервных болезней с медицинской генетикой и нейрохирургией

Ярославль.

Druzhinin D. S., Doctor of Medical Sciences, Associate Professor, Department of Nervous Diseases with Medical Genetics and Neurosurgery

Yaroslavl.

Медицинский центр «Жемчужина Подолья»РоссияMedical Center “Gemchuzhina Podolia"Russian FederationФГБОУ ВО «Ярославский государственный медицинский университет» Министерства здравоохранения Российской ФедерацииРоссияYaroslavl State Medical UniversityRussian Federation202309122023032Современная функциональная диагностика (4)4749Copyright © Халилова Т.Е., Дружинин Д.С., 20232023Халилова Т.Е., Дружинин Д.С.Khalilova T.E., Druzhinin D.S.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.med-alphabet.com/jour/article/view/3436

Нейролипоматоз — редко встречающаяся доброкачественная опухоль периферических нервов. Чаще вовлекаются нервы верхних конечностей, в большинстве случаев — срединные нервы в области запястного канала. Страдают в основном дети и люди молодого возраста. В статье описан случай фибролипоматозной гамартромы срединного нерва у пациента 24 лет, сопоставлено ультразвуковое изображение с результатами интраоперационного наблюдения. Несмотря на характерную клиническую и патоморфологическую картины этого состояния, вопросы диагностики и дифференциальной диагностики остаются актуальными. Особая роль отводится ультразвуку как неинвазивному, широко распространенному методу прижизненной диагностики состояния периферических нервов. Срединный нерв, благодаря своему поверхностному расположению, доступен для визуализации, а понимание ультразвуковой семиотики фибролипоматозной гамартомы позволит своевременно определять ее на этапе начальных клинических проявлений и избежать ненужных и усугубляющих неврологический дефицит методов обследования, таких как биопсия.

Neurolipomatosis is a rare benign tumor of peripheral nerves. The nerves of the upper extremities are more often involved, in most cases, the median nerves in the carpal canal. Children and young people suffer mainly. The article describes a case of fibrolipomatous hamarthroma of the median nerve in a 24-year-old patient, the ultrasound image is compared with the results of intraoperative observation. Despite the characteristic clinical and pathomorphological picture of this condition, the issues of diagnosis and differential diagnosis remain relevant. A special role is given to ultrasound as a non-invasive, widespread method of lifetime diagnosis of the condition of peripheral nerves. The median nerve, due to its superficial location, is available for visualization, and understanding the ultrasound semiotics of fibrolipomatous hamartoma will allow timely determination of it at the stage of initial clinical manifestations and avoid unnecessary and aggravating neurological deficits of examination methods such as biopsy.

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The authors declare that there are no conflicts of interest present.